Atrial Rhabdomyoma: A case Presentation and Review
Introduction:
Primary heart tumours are uncommon in pediatric with an occurrence about 0.28% in autopsy sequence. These tumours are the majority benign tumours (90%), but 10% are malignant. The most frequently primary benign pediatric heart tumour is rhabdomyoma, that frequently placed in the ventricles but they may also originate in the atriums and the atrioventricular junction. It includes more than 60% of the entire number of benign primary cardiac tumours during fetal and childhood . The cardiac teratoma and fibroma are next the most commonly primary cardiac tumors. 1-4
About a third of these tumors are detected at less than one year of age3 and the mean age of appearance is 12-13 years.5
Primary cardiac tumours is presented with the classic heart symptoms consequential from obstruction of blood flow, myocardial strain, and other symptoms. 424
Heart tumours primarily are arising in the pericardium, muscle layer and the internal lining of the heart.
Generally secondary malignant cardiac tumours are about15 times more common than primary malignant cardiac tumours [4].
The presenting manifestation depend on the dimension and site of the mass. The manifestation of a heart tumour in foetal life period includes dysrrhythmia, congestive heart failure (CHF), hydrops of fatal, and uncommonly stillbirth. In the postnatal life and infancy heart tumours can influence function of the nearby cardiac structures and leading to
Symptoms do not occur until the advanced stages of the disease has occurred, such as your physician hearing a heart murmur, and performing tests. Symptoms include
Reaching out to the American Cancer Society, as well as nurse practitioner Mary Hesdorffer. I become knowledgeable on the diagnosis of Mesothelioma. Mesothelioma comprises 3% of cancer diagnosis. It develops in the mesothelial cells in one’s body; cells that are protective lining for the body’s organs and cavities. The disease has five known forms. Four of the forms are malignant cancers, with one being benign. Malignant cancer grows and invades the surrounding tissues, were benign cancer does neither. Pleural Mesothelioma develops in the lining of the lungs, known as the pleura with 70% of diagnosis being this form. Peritoneal Mesothelioma develops in the lining of the abdominal cavity, known as the peritoneal membrane with 25% of diagnosis being this form. Pericardial Mesothelioma develops in the lining of the heart, known as the pericardium, with 5% of cases being pericardial. Testicular Mesothelioma develops in the tunica vaginalis of the testicles, being the most rare form with fewer than 100 documented cases. Benign Mesothelioma, only form were full recovery is the probable outcome, is a form of mesothelioma that develops in the pleura, difference being its stagnant.
Currently, it is believed that these tumors derive from subendocardial mesenchymal stem cells and can originate from any chamber and cardiac structure.(1) Approximately 80% of these tumors arise in the left atrium along the interatrial septum near the fossa ovalis. In contrast, myxomas arising from heart valves are extremely rare.(2,3) We review report the case of a patient with syncope who was found to have a mass implanted on mitral valve. In addition, we review 87 cases available in literature and discuss the clinicopathological features of these tumors.
the American Cancer Society there are benign tumors, which are rare and often develop in
Along with most things, a person can be born with an abnormal heart. One defect is called Shone’s Complex (syndrome, disorder, anomaly). Shone’s is a rare congenital heart disease affecting the left side of the heart. The disease consists of four defects; coarctation (narrowing) of the aorta, “parachute” mitral valve, supravalvular mitral membrane (SVMM), and valvular/subvalvular aortic stenosis. Coarctation of the aorta prevents blood flow to the body via the left ventricle. When two leaflets
The only hope of surviving this is a connection between the sides of the heart. Usually this connection closes a few days after birth, but in this case it doesn't. So the right side pumps all the blood out, but when it tries to come back through the left side the whole is closed. This can quickly cause death because of no blood circulation. Babies born with hypoplastic left heart syndrome are usually put on medicine right after birth so the hole doesn't close and the blood can keep
A 42-year-old woman in her third trimester of an otherwise uncomplicated pregnancy was referred with suspected fetal right ventricular (RV) structural abnormality. A fetal echocardiogram found a moderate-sized, broad-based outpouching from the RV anterior wall. Infant was born at 40 weeks gestation (birth weight 3.7 kg) and was asymptomatic with a normal electrocardiogram. Echocardiography demonstrated a poorly contracting, thin walled aneurysm of the basal, anterior RV free wall with qualitatively moderately depressed global RV dysfunction. Cardiac magnetic resonance (CMR) examination was requested to better characterize the lesion and quantify ventricular size and function.
Hypertrophic cardiomyopathy is an inherited disease that affects the cardiac muscle of the heart, causing the walls of the heart to thicken and become stiff. [1] On a cellular level, the sarcomere
HLHS first described in 1952 by Lev as the pathologic complex hypoplasia of the aortic tract. Hypoplasia of the aortic tract including hypoplasia of the aorta, hypoplasia of the aorta and VSD, hypoplasia of the aorta with aortic stenosis or atresia, and hypoplasia of the aorta with or without mitral stenosis. In 1958, Noonan and Nadas termed these lesions as “Hypoplastic left heart syndrome”. Noonan describes HLHS as a spectrum of cardiac abnormalities characterized by marked hypoplasia of the left ventricle and ascending aorta. The embryologic cause is not fully understood. It probably results from a familial inheritance and genetic disorder. Most infants are diagnosed in the first few hours or days of life.
Congenital heart defects (CHD) are birth defects that are considered the common in the United States. These defects affect a newborn child’s blood flow to and from the heart and sometimes can leave the heart lacking parts that make it necessary for the heart to do its job. According to the Centers for Disease Control and Prevention (CDC) (2014), 1 in 4 children born with a CHD is considered critical and will result in that child needing heart surgery or other similar procedures within the first years of its life. These CHD’s can range from Atrial Septal Defects, Coarctation of the aorta, Ebstien anomaly, Pulmanary artesia, Tetralogy of Fallot, Trancus Arteriosus, Hypoplastic Left Heart Syndrome, as well as many others (Centers for Disease Control and Prevention, 2014). The specific CHD that will be covered in detail will be the Hypoplastic Left Heart Syndrome (HLHS). HLHS accounts for nearly 960 congenital birth defects per year and
Tetrology of Fallot(TOF) is the most common prenatal congenital cyanotic heart disease accounts for about 1/3600 live births and about 7% to 10% of of all congenital heart disease and is the most common cause of cyanosis in the neonatal period1 , 2. Typical Tetralogy of Fallot (TOF) may be missed in Four chamber view. An abnormal Four chamber view is rarely seen in typical TOF cases . In the typical form of TOF the fetal echocardiography is often characterized by a normal four-chamber view, a subaortic Ventricular septal defect (VSD), Dilated over riding of aorta seen in a LVOT view, Pulmonary stenosis and an increased Aorta/Pulmonary artery ratio, minimal antegrade flow in the main pulmonary artery and the aortic flow originated from right and left ventricle. All pregnant women with low risk factors , suspected fetal cardiac anomalies and with increased risk factors should be analyzed by extended fetal echo during the level 2 scan (18 – 22 weeks scan ). It is also important to identify the side of the aortic arch, which is quite easier in the prenatal period in three vessel view . This will be useful if surgery is planned postnatally. Extracardiac abnormalities, such as midline defects, central nervous system and renal abnormalities may be found in fetuses with TOF. These extracardiac defects are associated with chromosomal abnormalities. When TOF is diagnosed, serial follow up scans at 5 – 6 weeks intervals are adviced to know about the growth of the
Tumors are one of the most feared diseases of our time. Many people upon hearing the word “tumor” immediately resonate to the conclusion of it being cancer, which is not necessarily true. Tumors fall into to two main types, benign and malignant. Although they are considerably different in tissue invasion, their nature that makes them distinct and symptoms, they are also quite similar in the way they recur in the same location, growth size and their health risks.
Congenital heart diseases (CHDs) are the most prevalent of all birth defects and the leading cause of death in the first year of life, (1) with an annual prevalence ranging from six to twelve affected infants per 1,000 live births. (2)
It is the second most common type of cancer found in children. Ewing's sarcoma typically occurs in people between 10 and 20 years old. However, it can occur at any age.
It is rarely found in children older than 10. This type of cancer accounts for about 7% of childhood cancers.