Case Analysis : Paediatric Cystic Fibrosis And The Vest Airway Clearance System
798 Words4 Pages
Paediatric Cystic Fibrosis and the Vest Airway Clearance System
The term endogenous is defined as “Having an internal cause or origin” (Oxford dictionary, 2015). These are diseases caused by the conditions already present within the body.
A hereditary disease is defined as “A disease or disorder that is inherited genetically” (Farlex, 2015). A hereditary disease is capable of being passed down through generation. Upon conception a child inherits a copy of genes from each parent, if defected they are predisposed to getting a disease. (Buzzle, 2015)
The following is an account of a 3 year old boy with a Cystic Fibrosis. Since birth the patient has been admitted to hospital for a bowel obstruction, poor growth, pancreatic insufficiency and recurrent lower respiratory tract infections. The Manual chest therapy (CBT) has been ineffective due to child being too weak to cough up pulmonary secretions. The patient’s physician has prescribed an oscillation device called the Vest System in a desperate attempt to mobilize the mucus.
Cystic fibrosis is a progressive, debilitating, inherited autosomal recessive disorder caused by a mutation to chromosome 7 this is required for producing the transmembrane conductance regulator (CFTR) responsible for regulating the sodium and chloride levels within a cell. (NHS, 2015) If the CFTR gene is defective or absent it creates an imbalance resulting in an accumulation of mucus leading to organ damage primarily