he noted atrophy of multiple muscles in patients with myotonia(Steinberg and Wagner 2008). Batten and Gibb of Britain also described wasting of stenomastoids, vastus internus and forearm muscles as well as difficulty releasing grasp in their 1909 paper (Batten and Gibb 1909). Fleischer in his genealogical examination was first to note that the gene does not cause disease in the first generation. This is followed by occurrence of more symptoms in the succeeding generations, starting with senile cataracts