Idiopathic Pulmonary Fibrosis

Cystic Fibrosis is a life threatening condition that causes severe damage to the lungs and digestive system. Developing this condition can change a person's entire life. Depending on the severity of the condition a person can be affected by mild symptoms such as shortness of breath, all the way to severe symptoms such as rectal prolapse, or even death. Screening is done on infants in all 50 states; therefore if a child has inherited Cystic Fibrosis it will be known in the first months of life. As professional staff members of a nursing community it will be necessary to help prepare the child and the family for the life of Cystic Fibrosis.

Accordingly, to this information of COPD: Coping with COPD from PubMed Health, this article provides the early stages, progression, coping and emergency plan and this disease affects family and friends. It is written answering the question, what to expect from COPD and how to manage this lung disease? A team of health care professionals, scientists and editors, and experts (Chronic obstructive pulmonary disease (COPD), 2015), provides education of how this disease may affect daily lives, how to live with this disease and what causes

What is Cystic Fibrosis? How does it affect people living with it? Cystic Fibrosis, also known as CF, is a life-threatening hereditary disease. It is inherited by a faulty cystic fibrosis transmembrane conductor (CFTR) gene from each parent (Kowalczyk, 2014, p. 74). This faulty gene makes a defective protein that does not work well and causes the body to produce sticky, thick mucus and very salty sweat("About CF: Causes, Signs & Symptoms of Cystic Fibrosis,"

This mucus build up also causes wheezing and difficulty breathing. Recently, it has become more common for individuals with cystic fibrosis to receive lung transplants during the end stages of lung disease. As mentioned, the symptoms of cystic fibrosis are life threatening, and the majority of deaths are the result of respiratory failure after battling lung diseases and infections that come as a result of the mucus build up. The life expectancy for an individual with cystic fibrosis ranges in the mid-thirties. Another symptom that comes as a result of cystic fibrosis is digestive issues. The thick mucus that affects the respiratory tract also often blocks the tubes that are crucial to digestion because they carry digestive enzymes. Without these digestive enzymes being transported to the small intestine, individuals with cystic fibrosis cannot fully absorb the nutrients they eat. These digestive issues lead to reduced weight gain and growth in individuals with cystic fibrosis as well as severe constipation. In some cases, the large intestine may begin to protrude, a symptom referred to as rectal prolapse, and may need to

Cystic Fibrosis affects 1 in every 2,500 children at birth. (ncbi.nlm.nih.gov) Cystic Fibrosis, or CF, is a genetic disorder. A genetic disorder is inherited, and is contributed to by both parents. (lung.org) Each parent has one abnormal gene. (lung.org) Cystic Fibrosis is where the body can not make, or it makes an abnormal version of the CFTR protein. CFTR is also known as cystic fibrosis transmembrane regulator. There are several symptoms, and causes of Cystic Fibrosis. These symptoms are diagnosed, according to what causes CF. Cystic Fibrosis is an inherited disease, that when after diagnosed, doctors will suggest treatments to help with the condition. Cystic Fibrosis is most common in white infants, but can

​Cystic fibrosis is a disease that is continually affecting children and adults in the United States. This is an inherited and life-threatening disease which affects many organs in the body. According to the Center for Disease Control, there are an estimated 30,000 people affected by this disease today. There are also approximately 2,500 babies born each year with Cystic fibrosis and unfortunately there are millions of people unaware they even carry the gene for this disease.

Cystic fibrosis is a genetic disorder caused by mutations of the cystic fibrosis transmembrane conductance regulator protein, which results in a defective chloride channels. Chloride is part of salt that helps transportation of water needed for thin, free flowing mucus. The main characterization of cystic fibrosis is thick, sticky mucus in the lungs, making breathing difficult and allowing pathogens to invade (Ratjen and Döring 2003). Airway mucus creates an iron limiting environment to prevent bacterial growth. However, Pseudomonas aeruginosa is a bacteria able to resist this airway mucus. This proposes a question as to why people with cystic fibrosis are prone to infection when exposed to the same pathogen as any healthy individuals. Research has suggested defective mucus clearance and biofilm formation could contribute to prolonged Pseudomonas aeruginosa infection in people with cystic fibrosis (Gi et al. 2015). Also, targeting cystic fibrosis transmembrane conductance regulator proteins to allow chloride transportation has been proven to decrease mucus volume and Pseudomonas aeruginosa infected tissue (Rowe et al. 2014). The above information suggests increased mucus volume causes prolonged infection in the lungs of cystic fibrosis patients. This paper will describe cystic fibrosis and will focus on the unanswered question as to why cystic fibrosis patients experience chronic infection in their lungs.

Cystic Fibrosis is a genetic disease. A person with CF has inherited two copies of the defective CF gene. One copy of the defective gene is inherited through each parent. A person with only one of these defective genes is considered a carrier but does not have CF. When two carriers have a child, there is a 25% chance the child will

The expected treatments include help from CF specialists, respiratory therapists, dieticians, and counselors (Story, 2015). Some of the strategies include pancreatic enzyme replacement, a well maintained high protein high sodium and low-fat diet, increased fluid, humidified air, bile salt replacement, postural drainage, fat soluble vitamin replacement, oxygen therapy, regular exercise, early and aggressive treatments with antibiotics (Story, 2015). The expected outcomes include a decrease in the severity of the symptoms this is a decrease in the respiratory infections. This can still be present and happen a lot and it can result in a lung transplant (McKinney et al., 2013). We want the family to adhere to the treatment plan after the teaching, have realistic goals set (McKinney et al., 2013). Parents role in the care is to help the child adhere to the treatment. Diet can be hard to manage for parents so meeting with a dietician and having the child help with meals may help with this. The parents should know how to administer medications, breathing treatments, reducing the risk for infections (McKinney et al., 2013). Having regular appointments with a doctor is also needed to make sure treatment is effective, infections are avoided. With the correct

Genetic diseases are the results of changes in an individual's DNA, usually inherited. An example of a fatal genetic disease is cystic fibrosis (also known as CF). This is the most common fatal genetic disease in the United States, over 30,000 people in the U.S. have cystic fibrosis and about 1,000 people are diagnosed each year. This disease attacks many different parts of the body, but the most affected area is the lungs. Cystic Fibrosis is genetic, has obvious symptoms, and is deadly.

An disease that can people can get that deal with enzymes is Cystic Fibrosis. Cystic Fibrosis is an inherited disease that can cause the body to produce mucus that is extremely thick and sticky. The reason why it is thicker than normal is because the disease affects the cell epithelium. The epithelium the the layer of cells that lines the passages in the body's organs. This disease that affect two organs are lungs and pancreas. The thickness of the mucus cause breathing and digestive problem. This also means the thicker the mucus have trouble moving out of the lungs which causes bacteria to remain in the organ which causes the infection.

Scientific name for this genetic mutation is the name of it itself which is cystic fibrosis. The CFTR gene is the gene that is mutated. The symptoms of this mutation are mucus that is abnormally thick and sticky that can build up and block airways. Cystic fibrosis was first discovered/observed in 1938. Dr. Dorothy Hansine Anderson is who first discovered cystic fibrosis. It was first discovered in North Carolina. People with cystic fibrosis must take one ampule of pulmozyme, pulmozyme is supplied in single-use ampules. It should be stored under refrigeration and protected from strong light. 2 interesting facts about cystic fibrosis is that it effects more than 30,000 children and adults in the United States. Worldwide it effects 70,000 people.

Some patients may experience episodes of acute respiratory worsening despite previous stability. НH ATS/ERS/JRS/ALAT 2011 Revised Diagnostic Criteria Нe diagnosis of IPF is based on the absence of a known cause of lung firosis computed tomography (CT) fidings and, in cases with CT abnormalities that are not classical for IPF, the use of pathological criteria [2].

Cystic fibrosis is an inherited disease that ultimately leads to death. It affects every racial group worldwide, but its prevalence varies from country to country. In those with cystic fibrosis, the lungs and digestive system are primarily affected by the disease. With the new developments in treatment and management, the 50 percent survival rate from the 1970’s has greatly improved, allowing patients to continue to live their lives longer than ever expected in the past. The new developments in prevention of exacerbations, therapy drugs and methods to preserve lung function have done great things to help patients extend their lives. Education is another important aspect of treating cystic fibrosis. For example, more the

COPD exhibits physiological symptoms such as dyspnea, chronic cough, cyanosis, weight loss, and wheezing. The disease process also exhibits psychological manifestations such as depression, difficulty with coping, altered body image disturbances, and anxiety. Inaccurate assessment of these symptoms could deter proper treatment of these patients or possibly worsen these patients’ conditions. According to McGinley’s (2014), “The role of nutrition in the management of COPD patients,” “Those patients identified as malnourished or at risk of malnutrition are more likely to be admitted to hospital, experience increased length of hospital stay, have earlier readmission rates and have a poorer prognosis. In particular to COPD, malnutrition can impair pulmonary