Medical Case Study: M. H. Sickle Cell Disease

Decent Essays
CHIEF COMPLAINT: Stated by the father “M.H. keep complaining of earache and on and off fever”
This is a 3-years-old African American male, who presented to the Pediatric Comprehensive Hemoglobinopathy clinic at the University of Michigan C.S. Mott Children's Hospital on 01/25/2017 for a routine follow up visit accompanied by his father. M.H. was diagnosed with Homozygous SS Sickle Cell Disease since birth. Since, his last clinic visit on 7/28/2016, M.H. has been admitted for partial splenectomy in 8/23/2016. Then, in 12/23/2016 his parents brought him to the emergency department in henry ford hospital for mild rhinorrhea, occasional productive cough, temperature of 99 Fahrenheit and pain in his left hand. During
…show more content…
His course has been complicated by one episode of dactylitis and two episodes of acute splenic sequestration. Therefore, he had a single lumen port placement surgery for chronic transfusion therapy. Also, he had a partial splenectomy in 8/23/2016. Mariano is maintained on Amoxicillin for prevention of further sickle cell complications. The first Acute sickle cell splenic sequestration crisis was in 7/9/2014 that involved Initial Hgb 5.8, PLT count 153, splenic palpation presents 2 finger breadths below the left costal margin. He received two 5 mL/kg antigen matched, leuko reduced packed red blood cell transfusions spaced with a number of hours between transfusions. He was discharged with Hgb of 8.5. The second splenic sequestration crisis was in 8/14/2014 with initial Hgb 5.0, PLT count 62 and the spleen was palpable 3 cm below the left costal margin. He received 1 packed red blood cell transfusion. Upon discharge Hgb 7.5 and the spleen tip was not palpable. In 12/6/2015 he was admitted to the hematology unit for three days due to fever 102, positive culture of Rhinovirus and viridans group streptococci, and right leg pain crisis. In 11/17/2015 he was admitted for 2 days for fever of 101, but blood cultures and chest X-ray were negative. Ultimately, in 8/23/2016 when he became 3-year-old, he had a partial splenectomy. He is maintained on Amoxicillin for prevention of further sickle cell
Get Access